Bilateral intracochlear schwannomas in a patient with no genetic or clinical features of neurofibromatosis type 2

Shannon Withers, S. K. Plontke, R. Boeddinghaus, J. Kuthubutheen, M. Atlas

Research output: Contribution to journalArticle

Abstract

Schwannomas of the eighth cranial nerve are benign tumours commonly found in the internal auditory meatus or in the cerebellopontine angle. In most cases, they arise from the inferior or vestibular portion of the vestibular nerve. Rarely, these tumours present in the inner ear and are then called intralabyrinthine schwannomas. Bilateral schwannomas are known in neurofibromatosis type 2 (NF2). Bilateral and ipsilateral, multilocular sporadic schwannomas of the eighth cranial nerve have been described as extremely rare findings. This report describes the first case of bilateral sporadic intracochlear schwannomas in a patient with no genetic or clinical features of NF2.

Translated title of the contributionBilateral intracochlear schwannomas in a patient with no genetic or clinical features of neurofibromatosis type 2
Original languageGerman
JournalHNO
DOIs
Publication statusE-pub ahead of print - 9 Oct 2019

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Neurofibromatoses
Neurilemmoma
Vestibulocochlear Nerve
Vestibular Nerve
Cerebellopontine Angle
Inner Ear
Neoplasms

Cite this

@article{95abc49ab2a844e596aa48ce80b68e79,
title = "Bilaterale intracochle{\"a}re Schwannome bei einer Patientin ohne genetische oder klinische Hinweise auf Neurofibromatose Typ 2",
abstract = "Schwannomas of the eighth cranial nerve are benign tumours commonly found in the internal auditory meatus or in the cerebellopontine angle. In most cases, they arise from the inferior or vestibular portion of the vestibular nerve. Rarely, these tumours present in the inner ear and are then called intralabyrinthine schwannomas. Bilateral schwannomas are known in neurofibromatosis type 2 (NF2). Bilateral and ipsilateral, multilocular sporadic schwannomas of the eighth cranial nerve have been described as extremely rare findings. This report describes the first case of bilateral sporadic intracochlear schwannomas in a patient with no genetic or clinical features of NF2.",
keywords = "Acoustic neuroma, Intracochlear schwannoma, Intralabyrinthine schwannoma, Sensorineural hearing loss, Vestibular schwannoma",
author = "Shannon Withers and Plontke, {S. K.} and R. Boeddinghaus and J. Kuthubutheen and M. Atlas",
year = "2019",
month = "10",
day = "9",
doi = "10.1007/s00106-019-00752-9",
language = "German",
journal = "HNO",
issn = "0017-6192",
publisher = "Springer",

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Bilaterale intracochleäre Schwannome bei einer Patientin ohne genetische oder klinische Hinweise auf Neurofibromatose Typ 2. / Withers, Shannon; Plontke, S. K.; Boeddinghaus, R.; Kuthubutheen, J.; Atlas, M.

In: HNO, 09.10.2019.

Research output: Contribution to journalArticle

TY - JOUR

T1 - Bilaterale intracochleäre Schwannome bei einer Patientin ohne genetische oder klinische Hinweise auf Neurofibromatose Typ 2

AU - Withers, Shannon

AU - Plontke, S. K.

AU - Boeddinghaus, R.

AU - Kuthubutheen, J.

AU - Atlas, M.

PY - 2019/10/9

Y1 - 2019/10/9

N2 - Schwannomas of the eighth cranial nerve are benign tumours commonly found in the internal auditory meatus or in the cerebellopontine angle. In most cases, they arise from the inferior or vestibular portion of the vestibular nerve. Rarely, these tumours present in the inner ear and are then called intralabyrinthine schwannomas. Bilateral schwannomas are known in neurofibromatosis type 2 (NF2). Bilateral and ipsilateral, multilocular sporadic schwannomas of the eighth cranial nerve have been described as extremely rare findings. This report describes the first case of bilateral sporadic intracochlear schwannomas in a patient with no genetic or clinical features of NF2.

AB - Schwannomas of the eighth cranial nerve are benign tumours commonly found in the internal auditory meatus or in the cerebellopontine angle. In most cases, they arise from the inferior or vestibular portion of the vestibular nerve. Rarely, these tumours present in the inner ear and are then called intralabyrinthine schwannomas. Bilateral schwannomas are known in neurofibromatosis type 2 (NF2). Bilateral and ipsilateral, multilocular sporadic schwannomas of the eighth cranial nerve have been described as extremely rare findings. This report describes the first case of bilateral sporadic intracochlear schwannomas in a patient with no genetic or clinical features of NF2.

KW - Acoustic neuroma

KW - Intracochlear schwannoma

KW - Intralabyrinthine schwannoma

KW - Sensorineural hearing loss

KW - Vestibular schwannoma

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U2 - 10.1007/s00106-019-00752-9

DO - 10.1007/s00106-019-00752-9

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