TY - JOUR
T1 - Adult hemiconvulsive hemiatrophy syndrome
T2 - a novel clinicoradiologic disorder in adults
AU - Kam, Ian
AU - Phatouros, Constantine
AU - Prentice, David
AU - Kho, Lay K
AU - Parizel, Paul
N1 - © 2023 Royal Australasian College of Physicians.
PY - 2023/7
Y1 - 2023/7
N2 - The association of focal motor seizures with cerebral hemiatrophy is a recognised rare paediatric syndrome known as 'hemiconvulsion, hemiatrophy and epilepsy' (HHE). To date, HHE has not been reported in adults. We present four adult patients with striking similarities to HHE, following alcohol withdrawal in chronic alcoholics. We document the imaging findings in the acute and subacute phases, discuss the underlying mechanisms and present a hypothesis regarding the pathophysiology.
AB - The association of focal motor seizures with cerebral hemiatrophy is a recognised rare paediatric syndrome known as 'hemiconvulsion, hemiatrophy and epilepsy' (HHE). To date, HHE has not been reported in adults. We present four adult patients with striking similarities to HHE, following alcohol withdrawal in chronic alcoholics. We document the imaging findings in the acute and subacute phases, discuss the underlying mechanisms and present a hypothesis regarding the pathophysiology.
UR - http://www.scopus.com/inward/record.url?scp=85165496154&partnerID=8YFLogxK
U2 - 10.1111/imj.16162
DO - 10.1111/imj.16162
M3 - Article
C2 - 37474458
SN - 1444-0903
VL - 53
SP - 1277
EP - 1283
JO - Internal Medicine Journal
JF - Internal Medicine Journal
IS - 7
ER -