• The University of Western Australia (M519), 35 Stirling Highway,

    6009 Perth

    Australia

  • 431 Citations
  • 10 h-Index
20102018
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  • 12 Similar Profiles
Mitochondrial Proteins Medicine & Life Sciences
RNA-Binding Proteins Medicine & Life Sciences
Mutation Medicine & Life Sciences
Leigh Disease Medicine & Life Sciences
RNA Medicine & Life Sciences
Transfer RNA Medicine & Life Sciences
Mitochondrial Genes Medicine & Life Sciences
Proteins Medicine & Life Sciences

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Research Output 2010 2018

  • 431 Citations
  • 10 h-Index
  • 17 Article
  • 1 Letter
  • 1 Doctoral Thesis
4 Citations (Scopus)

Concerted regulation of mitochondrial and nuclear non-coding RNAs by a dual-targeted RNase Z

Siira, S. J., Rossetti, G., Richman, T. R., Perks, K., Ermer, J. A., Kuznetsova, I., Hughes, L., Shearwood, A. M. J., Viola, H. M., Hool, L. C., Rackham, O. & Filipovska, A., 1 Oct 2018, In : EMBO Reports. 19, 10, e46198.

Research output: Contribution to journalArticle

Nuclear RNA
Untranslated RNA
Transfer RNA
MicroRNAs
Small Nucleolar RNA
2 Citations (Scopus)

Tighter Ligand Binding Can Compensate for Impaired Stability of an RNA-Binding Protein

Wallis, C. P., Richman, T. R., Filipovska, A. & Rackham, O., 15 Jun 2018, In : ACS Chemical Biology. 13, 6, p. 1499-1505 7 p.

Research output: Contribution to journalArticle

RNA-Binding Proteins
Ligands
Proteins
Mutation
Protein Engineering
7 Citations (Scopus)

Adult-onset obesity is triggered by impaired mitochondrial gene expression

Perks, K. L., Ferreira, N., Richman, T. R., Ermer, J. A., Kuznetsova, I., Shearwood, A-M. J., Lee, R. G., Viola, H. M., Johnstone, V. P. A., Matthews, V., Hool, L. C., Rackham, O. & Filipovska, A., Aug 2017, In : Science Advances. 3, 8, p. e1700677

Research output: Contribution to journalArticle

Open Access
Haploinsufficiency
Mitochondrial Genes
Obesity
Gene Expression
RNA
13 Citations (Scopus)

Biallelic Mutations in MRPS34 Lead to Instability of the Small Mitoribosomal Subunit and Leigh Syndrome

Lake, N. J., Webb, B. D., Stroud, D. A., Richman, T. R., Ruzzenente, B., Compton, A. G., Mountford, H. S., Pulman, J., Zangarelli, C., Rio, M., Bodaert, N., Assouline, Z., Sherpa, M. D., Schadt, E. E., Houten, S. M., Byrnes, J., McCormick, E. M., Zolkipli-Cunningham, Z., Haude, K., Zhang, Z. & 11 othersRetterer, K., Bai, R., Calvo, S. E., Mootha, V. K., Christodoulou, J., Rötig, A., Filipovska, A., Cristian, I., Falk, M. J., Metodiev, M. D. & Thorburn, D. R., 3 Aug 2017, In : American Journal of Human Genetics. 101, 2, p. 239-254 16 p.

Research output: Contribution to journalArticle

Open Access
Leigh Disease
Oxidative Phosphorylation
Mutation
Protein Subunits
Mitochondrial DNA
25 Citations (Scopus)

Hierarchical RNA Processing Is Required for Mitochondrial Ribosome Assembly

Rackham, O., Busch, J. D., Matic, S., Siira, S., Kuznetsova, I., Atanassov, I., Ermer, J., Shearwood, A-M., Richman, T., Stewart, J. B., Mourier, A., Milenkovic, D., Larsson, N. G. & Filipovska, A., 16 Aug 2016, In : Cell Reports. 16, 7, p. 1874-1890

Research output: Contribution to journalArticle

Open Access
RNA
Processing
Transfer RNA
Endoribonucleases
Ribonuclease P

Projects 2016 2017